JOMPAC
Journal of Medicine and Palliative Care

Journal of Medicine and Palliative Care (JOMPAC) is an open access scientific journal with independent, unbiased, and double-blind review under international guidelines. The purpose of JOMPAC is to contribute to the literature by publishing articles on health sciences and medicine.

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Case Report
Desmoid-type fibromatosis in the puerperium: a case report with pelvic exenteration
Abstract
Desmoid-type fibromatosis (DF) is a rare, locally aggressive soft tissue tumor with no metastatic potential but a high recurrence rate. We present the case of a 28-year-old postpartum woman who developed a rapidly enlarging pelvic mass, which was later confirmed as DF via imaging and biopsy. The initial management with chemotherapy and radiotherapy was unsuccessful, necessitating radical surgical intervention with pelvic exenteration. Given its association with hormonal changes, particularly during pregnancy and the postpartum period, DF poses significant diagnostic and therapeutic challenges. This case underscores the importance of early recognition, multidisciplinary management, and individualized treatment strategies to optimize patient outcomes.

Keywords : Desmoid fibromatosis, postpartum period, pelvic exenteration

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Article available in :
Volume 6, Issue 2, 2025
Page : 174-176
https://doi.org/10.47582/jompac.1648583
Article Information
Received : 28 Şub 2025
Accepted : 17 Mar 2025
Published : 23 Mar 2025
Corresponding Author :

Nevin Tüten: Department of Obstetrics and Gynecology, Kanuni Sultan Süleyman Training and Research Hospital, İstanbul, Turkiye

[email protected]
Citation : Yılmaz N, Turan Bakırcı I, Çetin Arslan H, Özkan ÖF, Yeşildal C. Desmoid-type fibromatosis in the puerperium: a case report with pelvic exenteration. J Med Palliat Care. 2025;6(2):174-176.

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