JOMPAC
Journal of Medicine and Palliative Care

Journal of Medicine and Palliative Care (JOMPAC) is an open access scientific journal with independent, unbiased, and double-blind review under international guidelines. The purpose of JOMPAC is to contribute to the literature by publishing articles on health sciences and medicine.

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The diagnosis and treatment of idiopathic pulmonary fibrosis
Abstract
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive fibrosing interstitial lung disease (ILD) of unknown cause. The prognosis of IPF is poor, respiratory failure is the most common cause of mortality. Velcro rales are typical on respiratory system examination. Clubbing is seen in 30-60% of IPF cases. There is no laboratory test specific to IPF. Usual interstitial pneumonia (UIP) pattern is seen in IPF. UIP features in high-resolution computed tomography (HRCT); peripheral subpleural bibasilar reticular opacities, honeycombing, traction bronchiectasis and interseptal thickening. It shows craniocaudal localization. Diagnosis of IPF; It is diagnosed by the combination of HRCT findings and clinical findings. Antifibrotic drugs (Pirfenidone and Nintedanib) slow down the progression of IPF and reduce the number of annual attacks and reduce the frequency of hospitalization.

Keywords : Idiopathic pulmonary fibrosis, usual interstitial pneumonia, antifibrotic drugs

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Article available in :
Volume 5, Issue 1, 2024
Page : 85-90
https://doi.org/10.47582/jompac.1418227
Article Information
Received : 11 Oca 2024
Accepted : 21 Oca 2024
Published : 29 Şub 2024
Corresponding Author :

Berna Akıncı Özyürek: Department of Chest Disease, Ankara Atatürk Sanatorium Training and Research Hospital, University of Health Sciences, Ankara, Turkiye

[email protected]
Citation : Akıncı Özyürek B. The diagnosis and treatment of idiopathic pulmonary fibrosis. J Med Palliat Care. 2024;5(1):85-90.

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